PKU, Sorbitol, & Galactose/Fructose Disorders
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Phenylketonuria (PKU) Phenylketonuria (PKU) is a genetic deficiency of either Phenylalanine Hydroxylase or its cofactor, Tetrahydrobiopterin (THB). This inhibits the conversion of Phenylalanine to …
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USMLE Biochemistry High Yield Rating List
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Dietary Carbohydrates and Health
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Tay Sachs Disease, Gaucher & Neiman-Pick
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Maltose - an overview
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PKU, Phenylketonuria, Galactosemia, Hereditary Fructose Intolerance & Sorbitol Diabetic Cataracts
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PKU, Sorbitol, & Galactose/Fructose Disorders
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Tagatose - an overview
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The genetic consequences of our sweet tooth
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Clinical Approach to Inborn Errors of Metabolism in Paediatrics