Nutrients, Free Full-Text
![Nutrients, Free Full-Text](https://pub.mdpi-res.com/nutrients/nutrients-09-00356/article_deploy/html/images/nutrients-09-00356-g001-550.jpg?1493372870)
Fructose is one of the main sweetening agents in the human diet and its ingestion is increasing globally. Dietary sugar has particular effects on those whose capacity to metabolize fructose is limited. If intolerance to carbohydrates is a frequent finding in children, inborn errors of carbohydrate metabolism are rare conditions. Three inborn errors are known in the pathway of fructose metabolism; (1) essential or benign fructosuria due to fructokinase deficiency; (2) hereditary fructose intolerance; and (3) fructose-1,6-bisphosphatase deficiency. In this review the focus is set on the description of the clinical symptoms and biochemical anomalies in the three inborn errors of metabolism. The potential toxic effects of fructose in healthy humans also are discussed. Studies conducted in patients with inborn errors of fructose metabolism helped to understand fructose metabolism and its potential toxicity in healthy human. Influence of fructose on the glycolytic pathway and on purine catabolism is the cause of hypoglycemia, lactic acidosis and hyperuricemia. The discovery that fructose-mediated generation of uric acid may have a causal role in diabetes and obesity provided new understandings into pathogenesis for these frequent diseases.
![](https://www.mdpi.com/nutrients/nutrients-10-01052/article_deploy/html/images/nutrients-10-01052-g001-550.jpg)
Department store Nutrients, Free Full-Text, analog scale
![](https://www.mdpi.com/nutrients/nutrients-12-02457/article_deploy/html/images/nutrients-12-02457-g001-550.jpg)
Nutrients, Free Full-Text, o que significa a fórmula y=c+i+g+(x-m
![](https://static.vecteezy.com/system/resources/previews/000/153/449/original/nutrition-facts-label-vector-templates.jpg)
Nutrition Facts Label Vector Templates 153449 Vector Art at Vecteezy
![](https://pub.mdpi-res.com/announcement/7345.jpeg?1706862781)
Nutrients An Open Access Journal from MDPI
![](https://pub.mdpi-res.com/nutrients/nutrients-15-02178/article_deploy/html/images/nutrients-15-02178-g001-550.jpg?1683094317)
978-0072556421 Pdf Download - Colaboratory
![](https://external-preview.redd.it/nutrients-free-full-text-high-dose-spermidine-v0-PxGmBOJD29DAgLBdaANmJv87Ry9OVodNbLO7NI6cmA4.jpg?auto=webp&s=de32a82b823400d48012e7c8de7bfffc058446ad)
Nutrients, Free Full-Text
![](https://www.mdpi.com/nutrients/nutrients-04-01622/article_deploy/html/images/nutrients-04-01622-g001-1024.png)
Nutrients, Free Full-Text
![](https://www.milkandhoneynutrition.com/wp-content/uploads/2022/04/nutrient-dense-foods-for-stable-blood-sugars-cover-400-%C3%97-400-px.png)
Nutrients, Free Full-Text, neuro linker in real life
![](https://www.hibobbie.com/cdn/shop/files/PDP-Routine-4.jpg?v=1705950475)
Organic Infant Formula
![](https://pub.mdpi-res.com/nutrients/nutrients-15-02808/article_deploy/html/images/nutrients-15-02808-g001-550.jpg?1687240310)
Free Rp Codes No Survey No Download No Password 2015 - Colaboratory
![](https://pub.mdpi-res.com/nutrients/nutrients-15-03097/article_deploy/html/images/nutrients-15-03097-g001-550.jpg?1689054355)
Black Survey Completer 2.0 Free - Colaboratory
![](https://pub.mdpi-res.com/nutrients/nutrients-13-03714/article_deploy/html/images/nutrients-13-03714-g001-550.jpg?1637823434)
Player Resource Consortium V3.6 Alpha - Colaboratory